Introduction: Biliary atresia is the main cause of death by hepatic failure and the main indication for liver transplant in children. Material and methods: Descriptive, observational, and retrospective study, including the patients with biliary atresia, diagnosed and treated between January 1, and December 31, We analyzed epidemiologic, clinical, biochemical, and image data, as well as registered complications and present status. Results: Eighteen patients were evaluated. The median age at time of Kasai portoenterostomy was 63 days of life, with better prognosis for those patients who had surgery before 72 days.
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Biliary Atresia - Clinical Series
Colestasis neonatal e infantil. Universidad de Los Andes. Universidad Nacional de Colombia. La incidencia de colestasis neonatal es de aproximadamente 1 de cada 2. En la tabla 2 se resume el comportamiento HNI. Es inusual en adultos. Su incidencia es de 1 por cada 2.
Atresia das vias biliares
Reporte de caso. Biliary atresia is an obstructive neonatal cholangiopathy of unknown etiology that produces damage to the parenchyma of the liver and to the intrahepatic and extrahepatic bile ducts. It is the most common cause of neonatal cholestasis and liver transplantation in the pediatric population. In most cases it manifests as an isolated malformation. This article presents the case of a 75 day old patient with biliary atresia associated with abdominal heterotaxy. Biliary atresia syndrome together with splenic malformation has been previously described, as have biliary atresia associated with anatomical malformations of the spleen, pancreas, and heart.